产品名称

GBA Antibody

产品货号

ABB6742

其他名称

Alglucerase; betaGC; GBA1; GCase; GCB; GLUC; Glucosylceramidase; Imiglucerase;

Gene ID

Human:P04062    

SwissPro

Human:http://www.uniprot.org/uniprot/P04062    

宿主种属

Rabbit IgG

应用范围

WB IHC

稀释比例

WB 1:500~1:2000 IHC 1:50~1:200

反应种属

Human Rat

克隆性

Monoclonal

免疫原

A synthesized peptide derived from human GBA

保存液

Rabbit IgG in phosphate buffered saline , pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. Store at +4°C short term. Store at -20°C long term. Avoid freeze / thaw cycle.

纯化方式

Affinity-chromatography

保存条件

-20

背景资料

60kDa

产品概述

Defects in GBA are the cause of Gaucher disease (GD) [MIM:230800]; also known as glucocerebrosidase deficiency. GD is the most prevalent lysosomal storage disease, characterized by accumulation of glucosylceramide in the reticulo-endothelial system.