产品名称

Galactosidase alpha Antibody

产品货号

ABF302329

基因名称

Galactosidase alpha

蛋白名称

Galactosidase alpha

其他名称

Alpha gal A; GALA; Galactosidase, alpha; GLA; Melibiase;

SwissPro

Human:P06280    

宿主种属

Rabbit

应用范围

WB IHC ICC/IF IP FC

稀释比例

WB 1:500~1:2000 IHC 1:50~1:200 ICC/IF 1:50~1:200 IP 1:50 FC 1:80

反应种属

Human

克隆性

Monoclonal

免疫原

A synthesized peptide derived from human Galactosidase alpha

特异性

Galactosidase alpha Antibody detects endogenous levels of total Galactosidase alpha

同种型

Rabbit IgG

保存液

Rabbit IgG in phosphate buffered saline , pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol. Store at +4°C short term. Store at -20°C long term. Avoid freeze / thaw cycle.

纯化方式

Affinity-chromatography

保存条件

-20°C/1 year

背景资料

46kDa

产品概述

Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.